A rare, virus associated tumor due to human T-cell leukemia virus type 1 or human T-cell lymphotropic virus type 1 (HTLV-1) and is characterized by the presence of anti-HTLV-1 antibodies, and malignant, mature, medium-sized T cells with condensed chromatin and polylobated nuclei. The malignant cells exhibit a mature CD4+ T cells phenotype and express CD2, CD5, CD25, CD45RO, HLA-DR, and T-cell receptor αβ. Presentation is heterogeneous and is typically of aggressive leukemia or lymphoma, variable skin eruptions, and visceral organ involvement.
Synonyms:
ATLL
This is just here as a test because I lose it
Term information
database
cross reference
- UMLS:C0023493 (E (Exact mapping: the two concepts are equivalent))
- ICD-10:C91.5 (- NTBT (ORPHA code's Narrower Term maps to a Broader Term). - Attributed (The ICD10 code is attributed by Orphanet).)
- MeSH:D015459 (E (Exact mapping: the two concepts are equivalent))
- MedDRA:10001413 (E (Exact mapping: the two concepts are equivalent))
definition citation
- Orphanet
expertlink
- https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=86875
hasDbXref
- MeSH:D015459
- UMLS:C0023493
- MedDRA:10001413
- ICD-10:C91.5
has age of onset
- http://www.orpha.net/ORDO/Orphanet_409948
has inheritance
- http://www.orpha.net/ORDO/Orphanet_409931
- http://www.orpha.net/ORDO/Orphanet_409941
has point prevalence range
- http://www.orpha.net/ORDO/Orphanet_409977
notation
- ORPHA:86875
part of
- http://www.orpha.net/ORDO/Orphanet_289635
- http://www.orpha.net/ORDO/Orphanet_178551
present in
- http://www.orpha.net/ORDO/Orphanet_409984
Term relations
Subclass of: