MyxofibrosarcomaGo to external page http://www.orpha.net/ORDO/Orphanet_79105
A rare soft tissue sarcoma characterized by a malignant, fibroblastic lesion with variably myxoid stroma, pleomorphism, and a distinctively curvilinear vascular pattern. The majority of tumors arise in the limbs including the limb girdles, more often in dermal/subcutaneous tissues than in the underlying fascia and skeletal muscle, and usually present as a slowly growing, painless mass. Depth of the lesion and tumor grade do not influence the high rate of local recurrence, while the percentage of metastasis and tumor-associated mortality are much higher in deep-seated and high-grade neoplasms.
Synonyms: Myxoid malignant fibrous histiocytoma Fibromyxosarcoma
- MedDRA:10066948 (E (Exact mapping: the two concepts are equivalent))
- ICD-10:C49.9 (- NTBT (ORPHA code's Narrower Term maps to a Broader Term). - Attributed (The ICD10 code is attributed by Orphanet).)
- UMLS:C3714524 (E (Exact mapping: the two concepts are equivalent))