Rhabdoid tumor (RT) is an aggressive pediatric soft tissue sarcoma that arises in the kidney, the liver, the peripheral nerves and all miscellaneous soft-parts throughout the body. RT involving the central nervous system (CNS) is called atypical teratoid rhabdoid tumor (ATRT; see this term).


Malignant rhabdoid tumor

This is just here as a test because I lose it

Term information

database cross reference
  • https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=69077
  • OMIM:613325
  • ICD-10:C49.9
  • UMLS:C0206743
  • OMIM:609322
  • MeSH:D018335
has age of onset
  • http://www.orpha.net/ORDO/Orphanet_409946
  • http://www.orpha.net/ORDO/Orphanet_409945
  • http://www.orpha.net/ORDO/Orphanet_409944
  • http://www.orpha.net/ORDO/Orphanet_409943
has annual incidence range
  • http://www.orpha.net/ORDO/Orphanet_409979
has inheritance
  • http://www.orpha.net/ORDO/Orphanet_409941
has point prevalence range
  • http://www.orpha.net/ORDO/Orphanet_409981
  • ORPHA:69077
part of
  • http://www.orpha.net/ORDO/Orphanet_3394
present in
  • http://www.orpha.net/ORDO/Orphanet_409991
  • http://www.orpha.net/ORDO/Orphanet_409984

Term relations

Subclass of: