A rare nervous system tumor characterized by cells phenotypically representing Schwann cells but containing melanosomes and expressing melanoma markers. The entity occurs as a non-psammomatous (typically affecting spinal nerves) or a psammomatous (also involving nerves of the intestinal tract and heart) variant. About 50% of psammomatous tumors are associated with Carney complex. Slightly over 10% of melanotic schwannomas follow a malignant course.

Synonyms: Isolated melanocytic schwannoma

This is just here as a test because I lose it

Term information

database cross reference
  • ICD-10:D36.1 (- NTBT (ORPHA code's Narrower Term maps to a Broader Term). - Attributed (The ICD10 code is attributed by Orphanet).)
expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=590539

hasDbXref

ICD-10:D36.1

has age of onset

http://www.orpha.net/ORDO/Orphanet_409949

http://www.orpha.net/ORDO/Orphanet_409948

http://www.orpha.net/ORDO/Orphanet_409947

http://www.orpha.net/ORDO/Orphanet_409946

has annual incidence range

http://www.orpha.net/ORDO/Orphanet_409981

has point prevalence range

http://www.orpha.net/ORDO/Orphanet_409981

notation

ORPHA:590539

part of

http://www.orpha.net/ORDO/Orphanet_3394

http://www.orpha.net/ORDO/Orphanet_252131

present in

http://www.orpha.net/ORDO/Orphanet_409991

Term relations

Subclass of: