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Hepatoblastoma

^ http://www.orpha.net/ORDO/Orphanet_449


Hepatoblastoma (HB) is a malignant hepatic tumor and is the most common pediatric liver cancer. It is characterized by anorexia, weight loss and an enlarged abdomen. HB is more common in patients with familial adenomatous polyposis (FAP), and can occur in patients with other pre-existing liver conditions. About 5 % of HB cases are associated with genetic factors, especially overgrowth syndromes, such as Beckwith-Wiedemann syndrome (BWS) or hemihypertrophy.

Term info

database cross reference
  • MedDRA:10062001 (E (exact mapping (the terms and the concepts are equivalent)))
  • MeSH:D018197 (E (exact mapping (the terms and the concepts are equivalent)))
  • UMLS:C0206624 (E (exact mapping (the terms and the concepts are equivalent)))
  • OMIM:114550 (NTBT (narrower term maps to a broader term))
  • ICD-10:C22.2 (E (exact mapping (the terms and the concepts are equivalent)))
hasDbXref

MedDRA:10062001, MeSH:D018197, UMLS:C0206624, OMIM:114550, ICD-10:C22.2

notation

ORPHA:449