A malignant hepatic tumor, typically affecting the pediatric population, arising mostly in an otherwise healthy liver. The most common signs are abdominal distension and abdominal mass. Sometimes patients present with anorexia, weight loss, fatigue. Most HBLs are sporadic, but some cases are associated with genetic factors, especially overgrowth syndromes, such as Beckwith-Wiedemann syndrome (BWS) or hemihypertrophy, and familial adenomatous polyposis (FAP).

This is just here as a test because I lose it

Term information

database cross reference
expertlink
  • https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=449
hasDbXref
  • MedDRA:10062001
  • MeSH:D018197
  • UMLS:C0206624
  • OMIM:114550
  • ICD-10:C22.2
has age of onset
  • http://www.orpha.net/ORDO/Orphanet_409946
  • http://www.orpha.net/ORDO/Orphanet_409945
  • http://www.orpha.net/ORDO/Orphanet_409944
has annual incidence average value
  • 0.019
  • 0.008
  • 0.009
  • 0.017
  • 0.028
  • 0.011
  • 0.022
  • 0.033
  • 0.023
  • 0.042
  • 0.031
  • 0.043
  • 0.021
  • 0.032
  • 0.004
  • 0.005
  • 0.046
  • 0.025
  • 0.02
has annual incidence range
  • http://www.orpha.net/ORDO/Orphanet_409979
has inheritance
  • http://www.orpha.net/ORDO/Orphanet_409941
has lifetime prevalence range
  • http://www.orpha.net/ORDO/Orphanet_409976
has point prevalence range
  • http://www.orpha.net/ORDO/Orphanet_409981
  • http://www.orpha.net/ORDO/Orphanet_409976
notation
  • ORPHA:449
part of
  • http://www.orpha.net/ORDO/Orphanet_306636
present in
  • http://www.orpha.net/ORDO/Orphanet_410119
  • http://www.orpha.net/ORDO/Orphanet_409984
  • http://www.orpha.net/ORDO/Orphanet_409991
  • http://www.orpha.net/ORDO/Orphanet_410100
  • http://www.orpha.net/ORDO/Orphanet_410147
  • http://www.orpha.net/ORDO/Orphanet_410224
  • http://www.orpha.net/ORDO/Orphanet_410169
  • http://www.orpha.net/ORDO/Orphanet_410026
  • http://www.orpha.net/ORDO/Orphanet_410014
  • http://www.orpha.net/ORDO/Orphanet_410113
  • http://www.orpha.net/ORDO/Orphanet_410047
  • http://www.orpha.net/ORDO/Orphanet_410168
  • http://www.orpha.net/ORDO/Orphanet_410157
  • http://www.orpha.net/ORDO/Orphanet_410205
  • http://www.orpha.net/ORDO/Orphanet_410007
  • http://www.orpha.net/ORDO/Orphanet_410128
  • http://www.orpha.net/ORDO/Orphanet_410192
  • http://www.orpha.net/ORDO/Orphanet_410060
  • http://www.orpha.net/ORDO/Orphanet_410073
  • http://www.orpha.net/ORDO/Orphanet_410193
  • http://www.orpha.net/ORDO/Orphanet_410050
  • http://www.orpha.net/ORDO/Orphanet_410097
  • http://www.orpha.net/ORDO/Orphanet_410198
  • http://www.orpha.net/ORDO/Orphanet_410065

Term relations

Subclass of: