Peripheral primitive neuroectodermal tumor
Go to external page http://www.orpha.net/ORDO/Orphanet_370348
A rare, aggressive, malignant, neoplastic disease characterized by a usually ill-defined, solid, multilobulated mass, frequently having necrosis, located on any site of the body (except the central nervous system), composed of small, round, poorly differentiated cells, with or without Homer-Wright rosettes, showing varying degrees of neuroectodermal differentiation. Manifestations are variable depending on location, with osteolytic destruction being common when arising from bone.
Synonyms:
Peripheral PNET
PPNET
Peripheral neuroepithelioma
This is just here as a test because I lose it
Term information
database
cross reference
- OMIM:612219 (NTBT (ORPHA code's Narrower Term maps to a Broader Term))
- UMLS:C0684337 (E (Exact mapping: the two concepts are equivalent))
- ICD-10:C71.9 (- NTBT (ORPHA code's Narrower Term maps to a Broader Term). - Index term (The ORPHA code is listed in the ICD10 Index).)
definition citation
- Orphanet
expertlink
- https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=370348
hasDbXref
- ICD-10:C71.9
- OMIM:612219
- UMLS:C0684337
has age of onset
- http://www.orpha.net/ORDO/Orphanet_409948
- http://www.orpha.net/ORDO/Orphanet_409947
- http://www.orpha.net/ORDO/Orphanet_409946
has inheritance
- http://www.orpha.net/ORDO/Orphanet_409941
has point prevalence range
- http://www.orpha.net/ORDO/Orphanet_409981
notation
- ORPHA:370348
part of
- http://www.orpha.net/ORDO/Orphanet_3394
- http://www.orpha.net/ORDO/Orphanet_223727
present in
- http://www.orpha.net/ORDO/Orphanet_409991
Term relations
Subclass of: