Peripheral primitive neuroectodermal tumor

Go to external page http://www.orpha.net/ORDO/Orphanet_370348


A rare, aggressive, malignant, neoplastic disease characterized by a usually ill-defined, solid, multilobulated mass, frequently having necrosis, located on any site of the body (except the central nervous system), composed of small, round, poorly differentiated cells, with or without Homer-Wright rosettes, showing varying degrees of neuroectodermal differentiation. Manifestations are variable depending on location, with osteolytic destruction being common when arising from bone.

Synonyms: Peripheral PNET PPNET Peripheral neuroepithelioma

This is just here as a test because I lose it

Term information

database cross reference
expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=370348

hasDbXref

ICD-10:C71.9

OMIM:612219

UMLS:C0684337

has age of onset

http://www.orpha.net/ORDO/Orphanet_409948

http://www.orpha.net/ORDO/Orphanet_409947

http://www.orpha.net/ORDO/Orphanet_409946

has inheritance

http://www.orpha.net/ORDO/Orphanet_409941

has point prevalence range

http://www.orpha.net/ORDO/Orphanet_409981

notation

ORPHA:370348

part of

http://www.orpha.net/ORDO/Orphanet_3394

http://www.orpha.net/ORDO/Orphanet_223727

present in

http://www.orpha.net/ORDO/Orphanet_409991