Extraskeletal Ewing sarcoma is a rare, poorly differentiated, highly malignant, soft tissue tumor, derived from neuroectoderm, that is morphologically indistinguishable from skeletal Ewing sarcoma but is located in extraosseous locations, with the most common being: chest wall, paravertebral region, abdominopelvic area (with predilection for the retroperitoneal space), gluteal region and lower extremities. Clinical presentation is highly variable and depends on tumor localization. Local recurrence is common and metastatic disease most frequently involves the bones and lungs.
Synonyms:
Extraskeletal Ewing tumor
Extraosseous Ewing sarcoma
EOE
Extraosseous Ewing tumor
This is just here as a test because I lose it
Term information
database
cross reference
- UMLS:C0279980 (E (Exact mapping: the two concepts are equivalent))
- OMIM:612219 (NTBT (ORPHA code's Narrower Term maps to a Broader Term))
- ICD-10:C49.9 (- NTBT (ORPHA code's Narrower Term maps to a Broader Term). - Attributed (The ICD10 code is attributed by Orphanet).)
definition citation
- Orphanet
expertlink
- https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=370334
hasDbXref
- UMLS:C0279980
- ICD-10:C49.9
- OMIM:612219
has age of onset
- http://www.orpha.net/ORDO/Orphanet_409948
- http://www.orpha.net/ORDO/Orphanet_409947
- http://www.orpha.net/ORDO/Orphanet_409946
has annual incidence average value
- 0.106
- 0.018
- 0.077
- 0.055
- 0.089
- 0.056
- 0.01
- 0.023
- 0.087
- 0.076
- 0.043
- 0.126
- 0.112
- 0.068
- 0.058
- 0.092
- 0.081
- 0.05
- 0.052
- 0.071
- 0.083
has annual incidence range
- http://www.orpha.net/ORDO/Orphanet_409979
- http://www.orpha.net/ORDO/Orphanet_409976
has inheritance
- http://www.orpha.net/ORDO/Orphanet_409941
notation
- ORPHA:370334
part of
- http://www.orpha.net/ORDO/Orphanet_3394
- http://www.orpha.net/ORDO/Orphanet_506219
present in
- http://www.orpha.net/ORDO/Orphanet_410119
- http://www.orpha.net/ORDO/Orphanet_410100
- http://www.orpha.net/ORDO/Orphanet_410147
- http://www.orpha.net/ORDO/Orphanet_410026
- http://www.orpha.net/ORDO/Orphanet_410169
- http://www.orpha.net/ORDO/Orphanet_410224
- http://www.orpha.net/ORDO/Orphanet_410047
- http://www.orpha.net/ORDO/Orphanet_410113
- http://www.orpha.net/ORDO/Orphanet_410157
- http://www.orpha.net/ORDO/Orphanet_410014
- http://www.orpha.net/ORDO/Orphanet_410168
- http://www.orpha.net/ORDO/Orphanet_410007
- http://www.orpha.net/ORDO/Orphanet_410205
- http://www.orpha.net/ORDO/Orphanet_410128
- http://www.orpha.net/ORDO/Orphanet_410060
- http://www.orpha.net/ORDO/Orphanet_410192
- http://www.orpha.net/ORDO/Orphanet_410073
- http://www.orpha.net/ORDO/Orphanet_410193
- http://www.orpha.net/ORDO/Orphanet_410050
- http://www.orpha.net/ORDO/Orphanet_410097
- http://www.orpha.net/ORDO/Orphanet_410198
- http://www.orpha.net/ORDO/Orphanet_410065