Extraskeletal Ewing sarcoma is a rare, poorly differentiated, highly malignant, soft tissue tumor, derived from neuroectoderm, that is morphologically indistinguishable from skeletal Ewing sarcoma but is located in extraosseous locations, with the most common being: chest wall, paravertebral region, abdominopelvic area (with predilection for the retroperitoneal space), gluteal region and lower extremities. Clinical presentation is highly variable and depends on tumor localization. Local recurrence is common and metastatic disease most frequently involves the bones and lungs.

Synonyms:

Extraskeletal Ewing tumor

Extraosseous Ewing sarcoma

EOE

Extraosseous Ewing tumor

This is just here as a test because I lose it

Term information

database cross reference
expertlink
  • https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=370334
hasDbXref
  • UMLS:C0279980
  • ICD-10:C49.9
  • OMIM:612219
has age of onset
  • http://www.orpha.net/ORDO/Orphanet_409948
  • http://www.orpha.net/ORDO/Orphanet_409947
  • http://www.orpha.net/ORDO/Orphanet_409946
has annual incidence average value
  • 0.106
  • 0.018
  • 0.077
  • 0.055
  • 0.089
  • 0.056
  • 0.01
  • 0.023
  • 0.087
  • 0.076
  • 0.043
  • 0.126
  • 0.112
  • 0.068
  • 0.058
  • 0.092
  • 0.081
  • 0.05
  • 0.052
  • 0.071
  • 0.083
has annual incidence range
  • http://www.orpha.net/ORDO/Orphanet_409979
  • http://www.orpha.net/ORDO/Orphanet_409976
has inheritance
  • http://www.orpha.net/ORDO/Orphanet_409941
notation
  • ORPHA:370334
part of
  • http://www.orpha.net/ORDO/Orphanet_3394
  • http://www.orpha.net/ORDO/Orphanet_506219
present in
  • http://www.orpha.net/ORDO/Orphanet_410119
  • http://www.orpha.net/ORDO/Orphanet_410100
  • http://www.orpha.net/ORDO/Orphanet_410147
  • http://www.orpha.net/ORDO/Orphanet_410026
  • http://www.orpha.net/ORDO/Orphanet_410169
  • http://www.orpha.net/ORDO/Orphanet_410224
  • http://www.orpha.net/ORDO/Orphanet_410047
  • http://www.orpha.net/ORDO/Orphanet_410113
  • http://www.orpha.net/ORDO/Orphanet_410157
  • http://www.orpha.net/ORDO/Orphanet_410014
  • http://www.orpha.net/ORDO/Orphanet_410168
  • http://www.orpha.net/ORDO/Orphanet_410007
  • http://www.orpha.net/ORDO/Orphanet_410205
  • http://www.orpha.net/ORDO/Orphanet_410128
  • http://www.orpha.net/ORDO/Orphanet_410060
  • http://www.orpha.net/ORDO/Orphanet_410192
  • http://www.orpha.net/ORDO/Orphanet_410073
  • http://www.orpha.net/ORDO/Orphanet_410193
  • http://www.orpha.net/ORDO/Orphanet_410050
  • http://www.orpha.net/ORDO/Orphanet_410097
  • http://www.orpha.net/ORDO/Orphanet_410198
  • http://www.orpha.net/ORDO/Orphanet_410065