Extraskeletal Ewing sarcoma is a rare, poorly differentiated, highly malignant, soft tissue tumor, derived from neuroectoderm, that is morphologically indistinguishable from skeletal Ewing sarcoma but is located in extraosseous locations, with the most common being: chest wall, paravertebral region, abdominopelvic area (with predilection for the retroperitoneal space), gluteal region and lower extremities. Clinical presentation is highly variable and depends on tumor localization. Local recurrence is common and metastatic disease most frequently involves the bones and lungs.

Synonyms: Extraskeletal Ewing tumor Extraosseous Ewing sarcoma EOE Extraosseous Ewing tumor

This is just here as a test because I lose it

Term information

database cross reference
expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=370334

hasDbXref

UMLS:C0279980

ICD-10:C49.9

OMIM:612219

has age of onset

http://www.orpha.net/ORDO/Orphanet_409948

http://www.orpha.net/ORDO/Orphanet_409947

http://www.orpha.net/ORDO/Orphanet_409946

has annual incidence average value

0.106

0.018

0.077

0.055

0.089

0.056

0.01

0.023

0.087

0.076

0.043

0.126

0.112

0.068

0.058

0.092

0.081

0.05

0.052

0.071

0.083

has annual incidence range

http://www.orpha.net/ORDO/Orphanet_409979

http://www.orpha.net/ORDO/Orphanet_409976

has inheritance

http://www.orpha.net/ORDO/Orphanet_409941

notation

ORPHA:370334

part of

http://www.orpha.net/ORDO/Orphanet_3394

http://www.orpha.net/ORDO/Orphanet_506219

present in

http://www.orpha.net/ORDO/Orphanet_410119

http://www.orpha.net/ORDO/Orphanet_410100

http://www.orpha.net/ORDO/Orphanet_410147

http://www.orpha.net/ORDO/Orphanet_410026

http://www.orpha.net/ORDO/Orphanet_410169

http://www.orpha.net/ORDO/Orphanet_410224

http://www.orpha.net/ORDO/Orphanet_410047

http://www.orpha.net/ORDO/Orphanet_410113

http://www.orpha.net/ORDO/Orphanet_410157

http://www.orpha.net/ORDO/Orphanet_410014

http://www.orpha.net/ORDO/Orphanet_410168

http://www.orpha.net/ORDO/Orphanet_410007

http://www.orpha.net/ORDO/Orphanet_410205

http://www.orpha.net/ORDO/Orphanet_410128

http://www.orpha.net/ORDO/Orphanet_410060

http://www.orpha.net/ORDO/Orphanet_410192

http://www.orpha.net/ORDO/Orphanet_410073

http://www.orpha.net/ORDO/Orphanet_410193

http://www.orpha.net/ORDO/Orphanet_410050

http://www.orpha.net/ORDO/Orphanet_410097

http://www.orpha.net/ORDO/Orphanet_410198

http://www.orpha.net/ORDO/Orphanet_410065