Synovial sarcoma is an aggressive soft tissue sarcoma (see this term), occurring most commonly in adolescents and young adults (15 to 40 years), usually localized near the large joints of the extremities but also in the head and neck, mediastinum and viscera (lung, kidney etc), clinically presenting as a deep seated swelling or a painful mass often with an initial indolent course and is characterized by its local invasiveness and a propensity to metastasize. The origin of synovial sarcoma is likely from multipotent mesenchymal cells and not synovium (contrary to its name).

Synonyms:

Synovialosarcoma

This is just here as a test because I lose it

Term information

database cross reference
  • ICD-10:C49.9 (- NTBT (ORPHA code's Narrower Term maps to a Broader Term). - Attributed (The ICD10 code is attributed by Orphanet).)
  • UMLS:C0039101 (E (Exact mapping: the two concepts are equivalent))
  • MedDRA:10042863 (E (Exact mapping: the two concepts are equivalent))
  • OMIM:300813 (E (Exact mapping: the two concepts are equivalent))
expertlink
  • https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3273
hasDbXref
  • UMLS:C0039101
  • ICD-10:C49.9
  • OMIM:300813
  • MedDRA:10042863
has age of onset
  • http://www.orpha.net/ORDO/Orphanet_409950
has inheritance
  • http://www.orpha.net/ORDO/Orphanet_409941
has point prevalence range
  • http://www.orpha.net/ORDO/Orphanet_409981
notation
  • ORPHA:3273
part of
  • http://www.orpha.net/ORDO/Orphanet_3394
present in
  • http://www.orpha.net/ORDO/Orphanet_409991