Synovial sarcoma is an aggressive soft tissue sarcoma (see this term), occurring most commonly in adolescents and young adults (15 to 40 years), usually localized near the large joints of the extremities but also in the head and neck, mediastinum and viscera (lung, kidney etc), clinically presenting as a deep seated swelling or a painful mass often with an initial indolent course and is characterized by its local invasiveness and a propensity to metastasize. The origin of synovial sarcoma is likely from multipotent mesenchymal cells and not synovium (contrary to its name).

Synonyms: Synovialosarcoma

This is just here as a test because I lose it

Term information

database cross reference
  • MedDRA:10042863 (E (Exact mapping: the two concepts are equivalent))
  • OMIM:300813 (E (Exact mapping: the two concepts are equivalent))
  • UMLS:C0039101 (E (Exact mapping: the two concepts are equivalent))
  • ICD-10:C49.9 (- NTBT (ORPHA code's Narrower Term maps to a Broader Term). - Attributed (The ICD10 code is attributed by Orphanet).)
expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3273

hasDbXref

UMLS:C0039101

ICD-10:C49.9

OMIM:300813

MedDRA:10042863

has age of onset

http://www.orpha.net/ORDO/Orphanet_409950

has inheritance

http://www.orpha.net/ORDO/Orphanet_409941

has point prevalence range

http://www.orpha.net/ORDO/Orphanet_409981

notation

ORPHA:3273

part of

http://www.orpha.net/ORDO/Orphanet_3394

present in

http://www.orpha.net/ORDO/Orphanet_409991