A rare soft tissue sarcoma characterized by a high-grade lesion occurring almost exclusively in adults, composed of bizarre polygonal, round, and spindle cells with evidence of skeletal muscle differentiation. Patients usually present with a rapidly growing, painful mass located in the deep soft tissues of the extremities, but also other anatomic regions. Prognosis is generally poor.

This is just here as a test because I lose it

Term information

database cross reference
  • UMLS:C0334480 (E (Exact mapping: the two concepts are equivalent))
  • ICD-10:C49.9 (NTBT (ORPHA code's Narrower Term maps to a Broader Term))
hasDbXref

ICD-10:C49.9

UMLS:C0334480

notation

ORPHA:293199