A rare soft tissue sarcoma characterized by a slowly growing, painless space-occupying lesion, composed of large, uniform, epitheloid cells arranged in solid nests and/or alveolar structures, separated by thin, sinusoidal vessels. The tumor mostly affects adolescents and young adults. Early metastasis, most commonly to the lung, bones, and brain, is a characteristic feature and relevant prognostic factor, together with age at presentation and tumor size, while histological features have no prognostic significance.

Synonyms: ASPS Alveolar soft part sarcoma

This is just here as a test because I lose it

Term information

database cross reference
expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=163699

hasDbXref

UMLS:C0206657

OMIM:606243

ICD-10:C49.9

MeSH:D018234

MedDRA:10001882

has age of onset

http://www.orpha.net/ORDO/Orphanet_409950

has inheritance

http://www.orpha.net/ORDO/Orphanet_409941

notation

ORPHA:163699

part of

http://www.orpha.net/ORDO/Orphanet_3394