Ewing sarcoma/peripheral primitive neuroectodermal tumor

Go to external page http://purl.obolibrary.org/obo/MONDO_0021038


A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms. [ NCIT:C27291 ]

This is just here as a test because I lose it

Term information

database cross reference
  • UMLS:C3536893 (MONDO:equivalentTo)
  • NCIT:C27291 (MONDO:equivalentTo)
definition

A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms.

exactMatch

http://linkedlifedata.com/resource/umls/id/C3536893

http://purl.obolibrary.org/obo/NCIT_C27291

has exact synonym

Ewing sarcoma family of tumors

EFTs

Ewing's family of tumours

Ewing's sarcoma/peripheral primitive neuroectodermal tumor

Ewing family of tumors

tumors of the Ewing's family

Ewing sarcoma/peripheral primitive neuroectodermal tumor

Ewing sarcoma/peripheral PNET

tumors of Ewing's family

Ewing's family of tumors

id

MONDO:0021038

Term relations

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