Scleroderma is a rare autoimmune connective tissue disorder characterized by abnormal hardening of the skin and, sometimes, other organs. It is classified into two main forms: localized scleroderma and systemic sclerosis (SSc), the latter comprising three subsets; diffuse cutaneous SSc (dcSSc), limited cutaneous SSc (lcSSc) and limited SSc (lSSc). [ Orphanet:801 ]

This is just here as a test because I lose it

Term information

database cross reference
  • HP:0100324 (MONDO:otherHierarchy)
  • NCIT:C26746 (MONDO:equivalentTo)
  • Orphanet:801 (MONDO:equivalentTo)
  • MedDRA:10039710 (Orphanet:801)
  • DOID:419 (MONDO:equivalentTo)
Subsets

ordo_group_of_disorders

closeMatch

http://identifiers.org/snomedct/156451000

http://identifiers.org/snomedct/287005009

http://identifiers.org/snomedct/267874003

http://identifiers.org/snomedct/201440007

http://identifiers.org/snomedct/268049000

http://identifiers.org/snomedct/128457007

http://identifiers.org/snomedct/201441006

http://linkedlifedata.com/resource/umls/id/C0852007

http://identifiers.org/snomedct/156454008

definition

Scleroderma is a rare autoimmune connective tissue disorder characterized by abnormal hardening of the skin and, sometimes, other organs. It is classified into two main forms: localized scleroderma and systemic sclerosis (SSc), the latter comprising three subsets; diffuse cutaneous SSc (dcSSc), limited cutaneous SSc (lcSSc) and limited SSc (lSSc).

exactMatch

http://identifiers.org/meddra/10039710

http://purl.obolibrary.org/obo/DOID_419

http://www.orpha.net/ORDO/Orphanet_801

http://purl.obolibrary.org/obo/NCIT_C26746

http://linkedlifedata.com/resource/umls/id/C0011644

has exact synonym

scleroderma

Scleroderma

dermatosclerosis

id

MONDO:0019340