Relapsing polychondritis (RP) is a rare, clinically heterogeneous, multisystemic inflammatory disease characterized by inflammation of the cartilage and proteoglycan rich structures leading to cartilage damage with joint, ocular and cardiovascular involvement. [ Orphanet:728 ]
Term information
- NCIT:C157268 (MONDO:equivalentTo)
- MESH:D011081 (Orphanet:728)
- MedDRA:10038304 (Orphanet:728)
- UMLS:C0032453 (Orphanet:728)
- ICD10:M94.1 (Orphanet:728)
- SCTID:72275000 (MONDO:equivalentTo)
- EFO:1001148 (MONDO:equivalentTo)
- ICD9:733.99 (i2s)
- DOID:2556 (MONDO:equivalentTo)
- GARD:0007417 (MONDO:equivalentTo)
- Orphanet:728 (MONDO:equivalentTo)
gard_rare, ordo_disease
Relapsing polychondritis (RP) is a rare, clinically heterogeneous, multisystemic inflammatory disease characterized by inflammation of the cartilage and proteoglycan rich structures leading to cartilage damage with joint, ocular and cardiovascular involvement.
http://purl.obolibrary.org/obo/DOID_2556
http://identifiers.org/snomedct/72275000
http://purl.obolibrary.org/obo/NCIT_C157268
http://www.orpha.net/ORDO/Orphanet_728
http://identifiers.org/meddra/10038304
http://linkedlifedata.com/resource/umls/id/C0032453
http://identifiers.org/mesh/D011081