Primary systemic amyloidosis (PSA) is a form of AL amyloidosis caused by the aggregation and deposition of insoluble amyloid fibrils derived from misfolded monoclonal immunoglobulin light chains usually produced by a plasma cell tumor and characterized by multiple organ involvement. [ Orphanet:314701 ]

This is just here as a test because I lose it

Term information

database cross reference
  • ICD10:E85.2 (Orphanet:314701)
  • ICD10:E85.3 (Orphanet:314701)
  • ICD10:E85.1 (Orphanet:314701)
  • UMLS:C0281479 (MONDO:equivalentTo)
  • UMLS:C0268380 (NCIT:C8299)
  • NCIT:C8299 (MONDO:equivalentTo)
  • SCTID:89449005 (MONDO:equivalentTo)
  • Orphanet:314701 (MONDO:equivalentTo)
  • ICD10:E85.0 (Orphanet:314701)
Subsets

ordo_clinical_subtype

definition

Primary systemic amyloidosis (PSA) is a form of AL amyloidosis caused by the aggregation and deposition of insoluble amyloid fibrils derived from misfolded monoclonal immunoglobulin light chains usually produced by a plasma cell tumor and characterized by multiple organ involvement.

exactMatch

http://identifiers.org/snomedct/89449005

http://linkedlifedata.com/resource/umls/id/C0268380

http://linkedlifedata.com/resource/umls/id/C0281479

http://www.orpha.net/ORDO/Orphanet_314701

http://purl.obolibrary.org/obo/NCIT_C8299

has exact synonym

systemic amyloidosis

systemic Immunoglobulin Light chain amyloidosis

systemic AL amyloidosis

id

MONDO:0017816

Term relations

Subclass of: