An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma). [ NCIT:C3714 ]

This is just here as a test because I lose it

Term information

database cross reference
  • DOID:6193 (MONDO:equivalentTo)
  • MedDRA:10015099 (Orphanet:293202)
  • ICD10:C49.9 (Orphanet:293202)
  • Orphanet:293202 (MONDO:equivalentTo)
  • ICDO:8804/3 (NCIT:C3714)
  • GARD:0010181 (MONDO:equivalentTo)
  • ONCOTREE:EPIS (MONDO:equivalentTo)
  • NCIT:C3714 (MONDO:equivalentTo)
  • UMLS:C0205944 (Orphanet:293202)
Subsets

gard_rare, ordo_disease

abbreviation
ES [ NCIT:C3714 ]

closeMatch

http://identifiers.org/snomedct/59238007

definition

An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma).

exactMatch

http://www.orpha.net/ORDO/Orphanet_293202

http://purl.obolibrary.org/obo/DOID_6193

http://identifiers.org/meddra/10015099

http://purl.obolibrary.org/obo/NCIT_C3714

http://linkedlifedata.com/resource/umls/id/C0205944

has exact synonym

epithelioid cell sarcoma

epithelioid sarcoma

ES

id

MONDO:0017387

seeAlso

https://rarediseases.info.nih.gov/diseases/10181/epithelioid-sarcoma

Term relations

Subclass of: