A benign, multifocal, nodular and well-circumscribed neoplasm usually seen as a congenital neoplasm or in the first year of life. It is characterized by a biphasic growth pattern and is composed of small, undifferentiated mesenchymal cells associated with branching thin-walled vessels and more mature neoplastic spindle cells with abundant eosinophilic cytoplasm in a collagenous stroma. [ NCIT:C3742 ]
Term information
- DOID:0080109 (MONDO:equivalentTo)
- Orphanet:2591 (MONDO:equivalentTo)
- OMIMPS:228550 (MONDO:equivalentTo)
- ONCOTREE:IMS (MONDO:equivalentTo)
- UMLS:C0206648 (NCIT:C3742)
- MESH:D018224 (MONDO:equivalentTo)
- GARD:0002998 (MONDO:equivalentTo)
- ICDO:8824/1 (NCIT:C3742)
- NCIT:C3742 (MONDO:equivalentTo)
- ICD10:D48.1 (Orphanet:2591)
gard_rare, ordo_disease
A benign, multifocal, nodular and well-circumscribed neoplasm usually seen as a congenital neoplasm or in the first year of life. It is characterized by a biphasic growth pattern and is composed of small, undifferentiated mesenchymal cells associated with branching thin-walled vessels and more mature neoplastic spindle cells with abundant eosinophilic cytoplasm in a collagenous stroma.
http://www.orpha.net/ORDO/Orphanet_2591
http://linkedlifedata.com/resource/umls/id/C0432284
http://purl.obolibrary.org/obo/DOID_0080109
http://identifiers.org/mesh/D018224
http://purl.obolibrary.org/obo/NCIT_C3742
http://linkedlifedata.com/resource/umls/id/C0206648
infantile hemangiopericytoma
multicentric myofibromatosis
myofibromatosis
infantile myofibromatosis