Evans syndrome is a rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology. [ Orphanet:1959 ]

This is just here as a test because I lose it

Term information

database cross reference
  • Orphanet:1959 (MONDO:equivalentTo)
  • UMLS:C0272126 (Orphanet:1959)
  • ICD10:D69.3 (Orphanet:1959)
  • ICD10:D69.41 (MONDO:equivalentTo)
  • MESH:C536380 (MONDO:equivalentTo)
  • ICD9:287.32 (i2s)
  • NCIT:C61284 (MONDO:equivalentTo)
  • DOID:8931 (MONDO:equivalentTo)
  • COHD:436956 (MONDO:equivalentTo)
  • GARD:0006389 (MONDO:equivalentTo)
  • SCTID:75331009 (MONDO:equivalentTo)
  • MedDRA:10053873 (Orphanet:1959)
Subsets

gard_rare, ordo_disease

closeMatch

http://identifiers.org/snomedct/191315003

definition

Evans syndrome is a rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

exactMatch

http://purl.obolibrary.org/obo/NCIT_C61284

http://identifiers.org/meddra/10053873

http://www.orpha.net/ORDO/Orphanet_1959

http://identifiers.org/mesh/C536380

http://purl.obolibrary.org/obo/DOID_8931

http://identifiers.org/snomedct/75331009

http://linkedlifedata.com/resource/umls/id/C0272126

has exact synonym

immune pancytopenia

autoimmune hemolytic anemia and autoimmune thrombocytopenia

Evans' syndrome

has related synonym

Evan syndrome

id

MONDO:0016030

seeAlso

https://rarediseases.info.nih.gov/diseases/6389/evans-syndrome