Nasal encephalocele is an extracranial herniation of intracranial contents (that maintain a connection to the subarachnoid space) into the fonticulus frontalis, presenting with nasal broadening and/or as a compressible, blue, pulsatile mass near the nasal bridge (that enlarges on crying or with jugular vein compression) or as an intranasal mass originating in the cribiform plate and that can cause nasal obstruction or respiratory distress. Hydrocephalus and increased intracranial pressure are also reported in some cases. [ Orphanet:141118 ]

This is just here as a test because I lose it

Term information

database cross reference
  • SCTID:65455002 (MONDO:equivalentTo)
  • ICD10:Q01.1 (Orphanet:141118)
  • Orphanet:141118 (MONDO:equivalentTo)
Subsets

ordo_clinical_subtype

definition

Nasal encephalocele is an extracranial herniation of intracranial contents (that maintain a connection to the subarachnoid space) into the fonticulus frontalis, presenting with nasal broadening and/or as a compressible, blue, pulsatile mass near the nasal bridge (that enlarges on crying or with jugular vein compression) or as an intranasal mass originating in the cribiform plate and that can cause nasal obstruction or respiratory distress. Hydrocephalus and increased intracranial pressure are also reported in some cases.

exactMatch

http://www.orpha.net/ORDO/Orphanet_141118

http://identifiers.org/snomedct/65455002

http://linkedlifedata.com/resource/umls/id/C0014066

id

MONDO:0015394

Term relations