autoimmune pulmonary alveolar proteinosis

Go to external page http://purl.obolibrary.org/obo/MONDO_0012579


Pulmonary alveolar proteinosis (PAP) is a rare lung disease characterized by the accumulation of a lipoproteinaceous substance in the distal air spaces which positively stains with periodic acid-Schiff (PAS). [ Orphanet:747 ]

This is just here as a test because I lose it

Term information

database cross reference
  • GARD:0007499 (MONDO:equivalentTo)
  • Orphanet:747 (OMIM:610910)
  • MESH:C567049 (MONDO:equivalentTo)
  • SCTID:707443007 (MONDO:equivalentTo)
  • ICD10:J84.0 (Orphanet:747)
  • OMIM:610910 (Orphanet:747)
  • UMLS:C1970472 (Orphanet:747)
Subsets

gard_rare, ordo_disease

abbreviation
APAP [ Orphanet:747 ]

abbreviation
PAP [ GARD:0007499 ]

conformsTo

http://purl.obolibrary.org/obo/mondo/patterns/autoimmune.yaml

definition

Pulmonary alveolar proteinosis (PAP) is a rare lung disease characterized by the accumulation of a lipoproteinaceous substance in the distal air spaces which positively stains with periodic acid-Schiff (PAS).

exactMatch

http://identifiers.org/omim/610910

http://identifiers.org/snomedct/707443007

http://linkedlifedata.com/resource/umls/id/C1970472

http://www.orpha.net/ORDO/Orphanet_747

http://identifiers.org/mesh/C567049

excluded from QC check

http://purl.obolibrary.org/obo/mondo/sparql/qc/mondo/qc-omim-subsumption.sparql

has exact synonym

APAP

autoimmune PAP

idiopathic PAP

iPAP

idiopathic pulmonary alveolar proteinosis

has related synonym

pulmonary alveolar proteinosis autoimmune

acquired pulmonary alveolar proteinosis

pulmonary alveolar lipoproteinosis acquired

PAP acquired

pulmonary alveolar lipoproteinosis, acquired

pulmonary alveolar proteinosis, acquired

pulmonary alveolar proteinosis acquired

pulmonary alveolar proteinosis, autoimmune

Pap, acquired

PAP

id

MONDO:0012579

seeAlso

https://rarediseases.info.nih.gov/diseases/7499/autoimmune-pulmonary-alveolar-proteinosis