Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal. [ Orphanet:679 ]

This is just here as a test because I lose it

Term information

database cross reference
  • ICD9:447.8 (i2s)
  • SCTID:400171002 (MONDO:equivalentTo)
  • ICD10:I77.8 (Orphanet:679)
  • UMLS:C0221011 (Orphanet:679)
  • MESH:D054853 (Orphanet:679)
  • OMIM:602248 (Orphanet:679)
  • Orphanet:679 (OMIM:602248)
  • GARD:0006249 (Orphanet-shared)
  • MedDRA:10064281 (Orphanet:679)
  • NCIT:C84835 (MONDO:equivalentTo)
Subsets

ordo_disease

definition

Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal.

exactMatch

http://purl.obolibrary.org/obo/NCIT_C84835

http://identifiers.org/mesh/D054853

http://www.orpha.net/ORDO/Orphanet_679

http://linkedlifedata.com/resource/umls/id/C0221011

http://identifiers.org/snomedct/400171002

http://identifiers.org/omim/602248

http://identifiers.org/meddra/10064281

has exact synonym

papulosis atrophican maligna

Köhlmeier-Degos disease

Kohlmeier-Degos-Delort-Tricort syndrome

Degos disease

Köhlmeier-Degos-Delort-Tricort syndrome

Kohlmeier-Degos disease

malignant atrophic papulosis

has related synonym

atrophic papulosis, malignant

Degos syndrome

papulosis, malignant atrophic

Degos's malignant atrophic papulosis

id

MONDO:0011208