Semantic dementia (SD) is a form of frontotemporal dementia (FTD), characterized by the progressive, amodal and profound loss of semantic knowledge (combination of visual associative agnosia, anomia, surface dyslexia or dysgraphia and disrupted comprehension of word meaning) and behavioral abnormalities, attributable to the degeneration of the anterior temporal lobes. [ Orphanet:100069 ]

This is just here as a test because I lose it

Term information

database cross reference
  • GARD:0010792 (Orphanet-shared)
  • UMLS:C1862937 (OMIM:600274)
  • OMIM:600274 (Orphanet:100069)
  • Orphanet:100069 (MONDO:equivalentTo)
  • ICD10:G31.0 (Orphanet:100069)
Subsets

ordo_disease

definition

Semantic dementia (SD) is a form of frontotemporal dementia (FTD), characterized by the progressive, amodal and profound loss of semantic knowledge (combination of visual associative agnosia, anomia, surface dyslexia or dysgraphia and disrupted comprehension of word meaning) and behavioral abnormalities, attributable to the degeneration of the anterior temporal lobes.

exactMatch

http://www.orpha.net/ORDO/Orphanet_100069

https://omim.org/entry/600274

excluded from QC check

http://purl.obolibrary.org/obo/mondo/sparql/qc/general/qc-single-child.sparql

has exact synonym

semantic variant PPA

semantic primary progressive aphasia

has related synonym

disinhibition-dementia-Parkinsonism-amyotrophy Complex

frontotemporal lobe dementia

Ftdp17

frontotemporal lobar Degeneration with Tau inclusions

Pick Complex

frontotemporal dementia

frontotemporal dementia with Parkinsonism

multiple system tauopathy with presenile dementia

Pallidopontonigral Degeneration

Ftld with Tau inclusions

FTD

Wilhelmsen-Lynch disease

dementia, frontotemporal, with Parkinsonism

id

MONDO:0010857