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Craniopharyngioma

^ http://www.ebi.ac.uk/efo/EFO_1000209


A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO) [ NCIT:C2964 ]

A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO) [ http://www.ebi.ac.uk/ontology/webulous#OPPL_pattern ]

Synonyms: Rathke's pouch tumor, cystoma, Rathke pouch neoplasm, Rathke's pouch neoplasm, craniopharyngioma (WHO grade I), craniopharyngioma, craniopharyngioma (morphologic abnormality), tumor of Rathke's pouch, Rathke pouch tumor, neoplasm of Rathke's pouch, craniopharyngioma, benign

Term info

database cross reference
  • MESH:D003397 (Orphanet:54595)
  • GARD:0010486 (Orphanet-shared)
  • NCIT:C2964 (MONDO:equivalentTo)
  • MONDO:0018907
  • NCIt:C2964 (http://www.ebi.ac.uk/ontology/webulous#OPPL_pattern)
  • UMLS:C0010276 (Orphanet:54595)
  • SCTID:189179009 (MONDO:kboom-pr-1.00/0.91/29.66)
  • MedDRA:10011318 (Orphanet:54595)
  • DOID:3840 (MONDO:equivalentTo)
  • ICD10:D44.4 (Orphanet:54595)
  • Orphanet:54595 (MONDO:equivalentTo)
  • ICD9:237.0 (i2s)
  • ICDO:9350/1 (NCIT:C2964)
Subsets

ordo_disease

closeMatch

http://identifiers.org/snomedct/40009002

exactMatch

http://identifiers.org/snomedct/189179009, http://identifiers.org/meddra/10011318, http://purl.obolibrary.org/obo/NCIT_C2964, http://purl.obolibrary.org/obo/DOID_3840, http://identifiers.org/mesh/D003397, http://purl.obolibrary.org/obo/Orphanet_54595, http://linkedlifedata.com/resource/umls/id/C0010276

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0015514

has related synonym

craniopharyngeal duct tumor, Dysodontogenic epithelial tumor, Adamantinomatous tumor

id

EFO:1000209