JSON

Pulmonary arterial hypertension associated with connective tissue disease

^ http://www.ebi.ac.uk/efo/EFO_0009196


Pulmonary arterial hypertension (PAH, see this term) associated with connective tissue disease (PAH-CTD) is a form of pulmonary arterial hypertension (PAH, see this term) characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of a connective tissue disease. [ Orphanet:275798 ]

Synonyms: pulmonary arterial hypertension associated with connective tissue disease, connective tissue disease-associated PAH, PAH associated with connective tissue disease

Term info

database cross reference
  • MONDO:0017151
  • UMLS:CN202578 (MONDO:equivalentTo)
  • ICD9:416.8 (i2s)
  • Orphanet:275798 (MONDO:equivalentTo)
  • ICD10:I27.2 (Orphanet:275798)
  • UMLS:C3697982 (MONDO:equivalentTo)
  • SCTID:697903007 (MONDO:kboom-pr-1.00/0.92/29.66)
Subsets

ordo_group_of_disorders

exactMatch

http://linkedlifedata.com/resource/umls/id/C3697982, http://purl.obolibrary.org/obo/Orphanet_275798, http://linkedlifedata.com/resource/umls/id/CN202578, http://identifiers.org/snomedct/697903007

id

EFO:0009196