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alveolar rhabdomyosarcoma

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Alveolar

A rapidly growing malignant mesenchymal neoplasm. It is characterized by the presence of round cells with myoblastic differentiation and a fibrovascular stroma resembling an alveolar growth pattern. The tumor usually presents in the extremities.

Synonyms: Alveolar Rhabdomyosarcomas, Alveolar rhabdomyosarcoma (morphologic abnormality), aveolar rhabdomyosarcoma, Alveolar rhabdomyosarcoma (disorder), ARMS, Rhabdomyosarcoma, Alveolar, Rhabdomyosarcomas, Alveolar

Term info

SNOMEDCT definition citation

SNOMEDCT:63449009, SNOMEDCT:404053004

bioportal provenance

ARMS[accessedResource: NCIt:C3749][accessDate: 05-04-2011], Alveolar rhabdomyosarcoma (morphologic abnormality)[accessedResource: SNOMEDCT:63449009][accessDate: 05-04-2011], Alveolar Rhabdomyosarcomas[accessedResource: MSH:D018232][accessDate: 05-04-2011], A rapidly growing malignant mesenchymal neoplasm. It is characterized by the presence of round cells with myoblastic differentiation and a fibrovascular stroma resembling an alveolar growth pattern. The tumor usually presents in the extremities.[accessedResource: NCIt:C3749][accessDate: 05-04-2011], Alveolar rhabdomyosarcoma (disorder)[accessedResource: SNOMEDCT:404053004][accessDate: 05-04-2011], Rhabdomyosarcoma, Alveolar[accessedResource: MSH:D018232][accessDate: 05-04-2011], Rhabdomyosarcomas, Alveolar[accessedResource: MSH:D018232][accessDate: 05-04-2011], A form of RHABDOMYOSARCOMA occurring mainly in adolescents and young adults, affecting muscles of the extremities, trunk, orbital region, etc. It is extremely malignant, metastasizing widely at an early stage. Few cures have been achieved and the prognosis is poor. "Alveolar" refers to its microscopic appearance simulating the cells of the respiratory alveolus. (Holland et al., Cancer Medicine, 3d ed, p2188)[accessedResource: MSH:D018232][accessDate: 05-04-2011], aveolar rhabdomyosarcoma[accessedResource: DOID:4051][accessDate: 05-04-2011]

term editor

Tomasz Adamusiak, James Malone

Term relations

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