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Catecholaminergic polymorphic ventricular tachycardia

^ http://www.orpha.net/ORDO/Orphanet_3286


Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder characterized by adrenergically induced ventricular tachycardia (VT) manifesting as syncope and sudden death.

Synonyms: Double tachycardia induced by catecholamines, CPVT, Malignant paroxysmal ventricular tachycardia, Bidirectional tachycardia induced by catecholamine, Multifocal ventricular premature beats

Term info

database cross reference
  • OMIM:615441 (BTNT (broader term maps to a narrower term))
  • ICD-10:I47.2 (Attributed)
  • OMIM:614916 (BTNT (broader term maps to a narrower term))
  • OMIM:604772 (E (exact mapping (the terms and the concepts are equivalent)))
  • ICD-10:I47.2 (NTBT (narrower term maps to a broader term))
  • UMLS:C1631597 (E (exact mapping (the terms and the concepts are equivalent)))
  • OMIM:611938 (BTNT (broader term maps to a narrower term))
  • OMIM:614021 (BTNT (broader term maps to a narrower term))
hasDbXref

OMIM:611938, OMIM:604772, UMLS:C1631597, OMIM:614021, OMIM:615441, ICD-10:I47.2, OMIM:614916

notation

ORPHA:3286