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Frontotemporal dementia

^ http://www.orpha.net/ORDO/Orphanet_282


Frontotemporal dementia (FTD) comprises a group of neurodegenerative disorders, characterized by progressive changes in behavior, executive dysfunction and language impairment, as a result of degeneration of the medial prefrontal and frontoinsular cortices. Four clinical subtypes have been identified: semantic dementia, progressive non-fluent aphasia, behavioral variant FTD and right temporal lobar atrophy (see these terms).

Synonyms: FTD

Term info

database cross reference
  • ICD-10:G31.0 (NTBT (narrower term maps to a broader term))
  • OMIM:607485 (BTNT (broader term maps to a narrower term))
  • OMIM:172700 (BTNT (broader term maps to a narrower term))
  • MedDRA:10068968 (E (exact mapping (the terms and the concepts are equivalent)))
  • ICD-10:G31.0 (Attributed)
  • OMIM:600795 (BTNT (broader term maps to a narrower term))
  • UMLS:C0338451 (E (exact mapping (the terms and the concepts are equivalent)))
  • MeSH:D057180 (E (exact mapping (the terms and the concepts are equivalent)))
  • OMIM:600274 (E (exact mapping (the terms and the concepts are equivalent)))
hasDbXref

OMIM:600274, ICD-10:G31.0, OMIM:600795, OMIM:607485, MedDRA:10068968, OMIM:172700, UMLS:C0338451, MeSH:D057180

notation

ORPHA:282