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PDBe Entry: 2q71 view

Uroporphyrinogen Decarboxylase G168R single mutant enzyme in complex with coproporphyrinogen-III
Summary
Header LYASEsearch
Method X-RAY DIFFRACTION
Experiment Resolution: 1.9 Å, R-factor: 16.4%, Free R-factor: 19.9%, Spacegroup: P 31 2 1
Released 19/06/2007, deposition: 05/06/2007, last revision: 24/02/2009
Authors Phillips, J.D.search; Whitby, F.G.search; Stadtmueller, B.M.search; Edwards, C.Q.search; Hill, C.P.search; Kushner, J.P.search
Primary citation Two Novel Uropophyrinogen Decarboxylase (URO-D) Mutations Causing Hepatoerythropoietic Porphyria (HEP)
TRANSL.RES.search vol:149, pag:85-91 (2007) [PubMed ID 17240319 ]search
Keywords Uroporphyrinogen Decarboxylase enzyme UROD G168R coproporphyrinogen-III product complexsearch, LYASEsearch
EC 4.1.1.37 ExPASy BRENDA search (A)
Organism Homo sapiens(human) 9606search(A)
UniProt Uroporphyrinogen decarboxylase (EC 4.1.1.37) (URO-D) (UPD) P06132search (A)
Solvent A
Related entries 2q6z, 1ry3
Polymers
Id Name Type UniProt Residues Observed
A Uroporphyrinogen decarboxylase Protein P06132 (DCUP_HUMAN)search
356 100%
Heterogens
Id Name Ligands
A COPROPORPHYRIN III CP3 search
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