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PDBe Entry: 1o7a view

HUMAN BETA-HEXOSAMINIDASE B
Summary
Header HYDROLASEsearch
Method X-RAY DIFFRACTION
Experiment Resolution: 2.25 Å, R-factor: 19.6%, Free R-factor: 23.6%, Spacegroup: P 31 2 1
Released 23/10/2003, deposition: 29/10/2002, last revision: 24/02/2009
Authors Maier, T.search; Strater, N.search; Schuette, C.search; Klingenstein, R.search; Sandhoff, K.search; Saenger, W.search
Primary citation The X-Ray Crystal Structure of Human Beta-Hexosaminidase B Provides New Insights Into Sandhoff Disease
J.MOL.BIOL.search vol:328, pag:669 (2003) [PubMed ID 12706724 ]search
Keywords HYDROLASEsearch, GLYCOSYL HYDROLASEsearch, HEXOSAMINIDASEsearch, LYSOSOMALsearch, SPHINGOLIPID DEGRADATIONsearch, SANDHOFF DISEASEsearch, BA8-BARRELsearch, GLYCOSIDASEsearch
EC 3.2.1.52 ExPASy BRENDA search (A B C D E F)
Organism Homo sapiens(human) 9606search(A B C D E F)
UniProt Beta-hexosaminidase subunit beta precursor (EC 3.2.1.52) (N-acetyl-beta-glucosaminidase subunit beta) (Beta-N-acetylhexosaminidase subunit beta) (Hexosaminidase subunit B) (Cervical cancer proto-oncogene 7 protein) (HCC-7) [Contains: Beta-hexosaminidase subunit beta chain B; Beta-hexosaminidase subunit beta chain A] P07686search (A B C D E F)
Solvent A, B, C, D, E, F
Related entries 1qbd
Polymers
Id Name Type UniProt Residues Observed
A, B, C, D, E, F BETA-HEXOSAMINIDASE BETA CHAIN Protein P07686 (HEXB_HUMAN)search
515 93%
Heterogens
Id Name Ligands
A, B, C, D, E, F 2-ACETAMIDO-2-DEOXY-D-GLUCONO-1,5-LACTONE GDL search
A, B, C, D, E, F SUGAR (2-MER) NAG search
A, B, C, E, F SUGAR (N-ACETYL-D-GLUCOSAMINE) NAG search
A, B, C, E, F 1,2-ETHANEDIOL EDO search
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