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PDBe Entry: 1o7a 
HUMAN BETA-HEXOSAMINIDASE B
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HYDROLASE
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X-RAY DIFFRACTION
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Resolution: 2.25 Å, R-factor: 19.6%, Free R-factor: 23.6%, Spacegroup: P 31 2 1
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23/10/2003, deposition: 29/10/2002, last revision: 24/02/2009
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Maier, T. ; Strater, N. ; Schuette, C. ; Klingenstein, R. ; Sandhoff, K. ; Saenger, W.
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The X-Ray Crystal Structure of Human Beta-Hexosaminidase B Provides New Insights Into Sandhoff Disease J.MOL.BIOL. vol:328, pag:669 (2003) [PubMed ID 12706724 ]
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HYDROLASE , GLYCOSYL HYDROLASE , HEXOSAMINIDASE , LYSOSOMAL , SPHINGOLIPID DEGRADATION , SANDHOFF DISEASE , BA8-BARREL , GLYCOSIDASE
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3.2.1.52 ExPASy BRENDA (A B C D E F)
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Homo sapiens(human) 9606 (A B C D E F)
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Beta-hexosaminidase subunit beta precursor (EC 3.2.1.52) (N-acetyl-beta-glucosaminidase subunit beta) (Beta-N-acetylhexosaminidase subunit beta) (Hexosaminidase subunit B) (Cervical cancer proto-oncogene 7 protein) (HCC-7) [Contains: Beta-hexosaminidase subunit beta chain B; Beta-hexosaminidase subunit beta chain A] P07686 (A B C D E F)
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A, B, C, D, E, F
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1qbd
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| A, B, C, D, E, F |
BETA-HEXOSAMINIDASE BETA CHAIN |
Protein |
P07686 (HEXB_HUMAN)
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515 |
93% |
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| A, B, C, D, E, F |
2-ACETAMIDO-2-DEOXY-D-GLUCONO-1,5-LACTONE |
GDL
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| A, B, C, D, E, F |
SUGAR (2-MER) |
NAG
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| A, B, C, E, F |
SUGAR (N-ACETYL-D-GLUCOSAMINE) |
NAG
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| A, B, C, E, F |
1,2-ETHANEDIOL |
EDO
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